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| 14.4 |
The emergence of bone cells |
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Under the extremes of pressure, het and
climactic conditions of earlier periods of Earth, the bone cell is the
emergence of yet another specialized cell from the "proto skin" cells
hundreds of millions of years ago. In not only providing the internal strength
and support to withstand tremendous pressures, this type of cell created
ultimately the "perfect" universe for cells- one tightly protected
from any external extreme elements. In such environments, some of the most
specialized cells of all accomplished the task of creating new semi-complete
cells. |
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BONE is a rigid body tissue
consisting of cells embedded in an abundant, hard intercellular material. The
two principal components of this material, collagen and calcium phosphate,
distinguish bone from such other hard tissues as chitin, enamel, and shell. |
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The functions of bone include (1)
structural support for the mechanical action of soft tissues, such as
contraction of muscles, expansion of lungs; (2) protection of soft parts, as by
the brain case; (3) provision of a protective site for specialized tissues such
as the blood-forming system (bone marrow); and (4) a mineral reservoir or sink,
whereby endocrine systems regulate the level of calcium and phosphate in the
circulating body fluids. |
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| 14.4.1
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Evolutionary origin and significance
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Bone is found only in vertebrates, and, among modern vertebrates, only in bony
fish and higher classes. Although fossil ancestors of the elasmobranchs and
cyclostomes had armoured head cases, serving largely a protective function,
which appear to have been true bone, modern cyclostomes have only an
endoskeleton, or inner skeleton, of non calcified cartilage, and elasmobranchs,
a skeleton of calcified cartilage. Although a rigid endoskeleton performs
obvious body supportive functions for land-living vertebrates, it is doubtful
that bone offered any such mechanical advantage to the teleost (bony fish) in
which it first appeared, for in a supporting aquatic environment, great
structural rigidity is not essential for maintaining body configuration. The
sharks and rays are superb examples of mechanical engineering efficiency, and
their perseverance from the Devonian attests to the suitability of their
non bony endoskeleton. |
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In modern vertebrates true bone is found only in animals also capable of
controlling the osmotic and ionic composition of their internal fluid
environment. |
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Marine invertebrates exhibit interstitial fluid compositions essentially the
same as that of the surrounding sea water. Early signs of regulability are seen
in cyclostomes and elasmobranchs, but only at or above the level of true bone
fishes does the composition of the internal body fluids become constant. The
mechanisms involved in this regulation are many and complex and include both
the kidney and the gills. Fresh and marine waters provide abundant calcium, but
only traces of phosphate, and, because relatively high levels of phosphate are
characteristic of the body fluids of higher vertebrates, it seems likely that a
large, readily available internal phosphate reservoir would confer significant
independence of external environment on bony vertebrates. With the emergence of
terrestrial forms, the availability of calcium regulation became equally
significant. Along with the kidney and the various component glands of the
endocrine system, bone has contributed to development of internal fluid
homeostasis--the maintenance of a constant chemical composition. This was a
necessary step for emergence of land-living vertebrates. Moreover, out of the
buoyancy of water, structural rigidity of bone afforded mechanical advantages
that are the most obvious features of the modern vertebrate skeleton. |
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| 14.4.2 |
Chemical composition and physical
properties |
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Depending upon species, age, and type of bone, the
bone cells represent 1-15 percent of the volume of bone, but in mature bone in
most higher animals usually they represent 1-5 percent. The nonliving
intercellular material consists of an organic component, collagen (a fibrous
protein arranged in long strands or bundles similar in structure and
organization to the collagen of ligaments, tendons, and skin), with small
amounts of protein polysaccharides, mucopolysaccharides chemically bound to
protein and dispersed within and around the collagen fibre bundles, and an
inorganic mineral component in the form of innumerable rod-shaped crystals with
diameters on the order of 50 and lengths from 200 to 2,000 . These crystals
are arranged parallel with the long axes of collagen bundles and many actually
lie in voids within the bundles themselves. Organic material comprises 50
percent of the volume and 30 percent of the dry weight of the intercellular
composite, and mineral the remainder. The major minerals are calcium and
phosphate, present in proportions ranging from 1.4:1 to 2.1:1. When first
deposited, mineral is crystallographically amorphous but with maturation
becomes typical of the apatite minerals, the major component being
hydroxyapatite, Ca10(PO4)6(OH)2. Carbonate is also present, in amounts varying
from 4 percent of bone ash in fish and 8 percent in most mammals to more than
13 percent in the turtle, and occurs in two distinct phases, calcium carbonate
and a carbonate apatite. Except for that associated with its cellular elements,
there is little free water in adult mammalian bone (approximately 8 percent of
total volume). As a result, diffusion from surfaces into the interior of the
intercellular substance occurs at the slow rates more typical of diffusion from
surfaces of solids than within liquids. |
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The structural role of the skeleton depends on the hardness, strength, and
rigidity of bone. The mineral crystals are responsible for hardness, rigidity,
and the great compressive strength of bone, but they share with other
crystalline materials a great weakness in tension, arising from the tendency
for stress to concentrate about defects and for these defects to propagate. On
the other hand, the collagen fibrils of bone possess high elasticity, little
compressive strength, and considerable intrinsic tensile strength. The tensile
strength of bone depends, however, not on collagen alone but on the intimate
association of mineral with collagen, which confers on bone many of the general
properties exhibited by two-phase materials such as fibre glass and bamboo. In
such materials the dispersion of a rigid but brittle material in a matrix of
quite different elasticity prevents the propagation of stress failure through
the brittle material and hence allows a closer approach to the theoretical
limiting strength of single crystals. |
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The fine structure of bone has thus far frustrated
attempts to determine the true strength of the mineral-matrix composite at the
"unit" structural level. Compact bone specimens have been found to have tensile
strength in the range of 700-1,400 kilograms per square centimetre
(10,000-20,000 pounds per square inch), and compressive strengths in the range
of 1,400-2,100 kilograms per square centimetre (20,000-30,000 pounds per square
inch). These values are of the same general order as for aluminum or mild
steel, but bone has an advantage over such materials in that it is considerably
lighter. The great strength of bone exists principally along its long axis and
hence roughly parallel both to the collagen fibre axis and to the long axis of
the mineral crystals. |
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Although apparently stiff, bones exhibit a
considerable degree of elasticity, which is important to the skeleton's ability
to withstand impact. Estimates of modulus of elasticity of bone samples are of
the order of 420 to 700 kilograms per square centimetre (6,000 to 10,000 pounds
per square inch), a value very much less than steel, for example, indicating
much greater elasticity of bone. Perfect elasticity exists with loads up to 30
to 40 percent of breaking strength; above this, creep occurs, presumably along
natural defects within the bony structure. The modulus of elasticity in bone is
strikingly dependent upon the rate at which loads are applied, bones being
stiffer during rapid deformation than during slow; this behaviour suggests an
element of viscous flow during deformation. |
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As might be anticipated from consideration of the
two-phase composition of bone, variation in the mineral-collagen ratio leads to
change in physical properties: less mineral tends ultimately to greater
flexibility, and more mineral to increased brittleness. Optimal ratios, as
reflected in maximal tensile strength, are observed at an ash content of
approximately 66 percent, a value that is characteristic of the weight-bearing
bones of mammals |
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| 14.4.3 |
Bone morphology |
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Grossly, bone tissue is organized into a variety of shapes and configurations
adapted to the function of the bone concerned: broad, flat plates, such as
scapula, as anchors for large muscle masses, or hollow, thick-walled tubes,
such as femur, radius, ulna, for supporting weight or for use as a lever arm.
These different types of bone are distinguished more by their external shape
than by their basic structure. |
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In all bones the basic bone has an exterior layer, termed cortex, that is
smooth, dense, continuous, and of varying thickness. In its interior, bony
tissue is arranged in a network of intersecting plates and spicules, varying in
amount in different bones, enclosing spaces filled with blood vessels and
marrow. This honeycombed bone is termed cancellous, and the plates and spicules
trabeculae. In mature bone, trabeculae are arranged in an orderly pattern that
provides continuous units of bony tissue aligned parallel with the lines of
major compressive or tensile force. Trabeculae thus provide a complex series of
cross-braced interior struts so arranged as to give maximal rigidity with
minimal material. |
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Bones such as vertebrae, subject to primarily compressive or tensile forces,
usually have thin cortices and provide necessary structural rigidity through
trabeculae; whereas bones such as the femur, subject to prominent bending,
shear, or torsional forces, usually have thick cortices, a tubular
configuration, and a continuous cavity running through their centres (medullary
cavity). The cortical material of tubular bones is termed compact bone and
differs in a number of fine structural details from cancellous bone. |
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Long bones, distinctive of the body's extremities, exhibit a number of gross
structural features in common. The central region of the bone (diaphysis) is
the most clearly tubular. At one or commonly both ends the diaphysis flares
outward and assumes a predominantly cancellous internal structure. This region
(metaphysis) functions to transfer loads from weight-bearing joint surfaces to
the diaphysis. Finally, at the end of a long bone is a region known as an
epiphysis, which exhibits a cancellous internal structure and which comprises
the bony substructure of the joint surface. Prior to full skeletal maturity the
epiphysis is separated from the metaphysis by a cartilaginous plate, the growth
plate or physis; in bones with complex articulations (such as the humerus at
its lower end) or bones with multiple protuberances (such as the femur at its
upper end) there may be several separate epiphyses, each with its growth plate. |
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| 14.4.4 |
Four types of cells in bone |
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Microscopically, bone consists of hard, apparently homogeneous intercellular
material, within or upon which can be found four characteristic cell types:
osteoblast, osteocyte, osteoclast, and undifferentiated bone mesenchymal cells.
The osteoblast is responsible for the synthesis and deposition on bone surfaces
of the protein matrix of new intercellular material. The osteocyte is an
osteoblast that has been trapped within intercellular material, residing in a
cavity (lacuna) and communicating with other osteocytes as well as with free
bone surfaces by means of extensive filamentous protoplasmic extensions that
occupy long, meandering channels (canaliculi) through the bone substance. With
the exception of certain higher orders of modern fish, all bone, including
primitive vertebrate fossil bone, exhibits an osteocytic structure. Osteoclasts
are usually large, multinucleated cells that, working from bone surfaces,
resorb bone by direct chemical and enzymatic attack. Undifferentiated
mesenchymal cells of the bone reside in the loose connective tissue between
trabeculae, along vascular channels, and in the condensed fibrous tissue
covering the outside of the bone (periosteum); they give rise under appropriate
stimuli to either osteoblasts or osteoclasts. |
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Depending on how the protein fibrils and osteocytes of bone are arranged, bone
is of two major types: woven, in which collagen bundles and the long axes of
the osteocytes are randomly oriented, and lamellar, in which both the fibrils
and osteocytes are aligned in clear layers. In lamellar bone the layers
alternate every few microns, and the primary direction of the fibrils shifts
approximately 90. In compact bone of many mammalian species, lamellar bone is
further organized into units known as osteons, or haversian systems, which
consist of concentric cylindrical lamellar elements several millimetres long
and 0.2-0.3 millimetre (0.008-0.012 inch) in diameter. Osteons exhibit a gently
spiral course oriented along the axis of the bone. In their centre is a canal
(haversian canal) containing one or more small blood vessels, and at their
outer margins is a boundary layer known as a "cement line," which serves both
as a means of fixation for new bone deposited on an old surface and as a
diffusion barrier. Osteocytic processes do not penetrate the cement line, and
hence these barriers constitute the outer envelope of a nutritional unit,
osteocytes on opposite sides of a cement line deriving their nutrition from
different vascular channels. Cement lines are found in all types of bone, as
well as in osteons, and in general they indicate lines at which new bone was
deposited on an old surface. |
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In a typical long bone, blood is supplied by three
separate systems: nutrient artery, periosteal vessels, and epiphyseal vessels.
The diaphysis and metaphysis are nourished primarily by the nutrient artery,
which passes through the cortex into the medullary cavity and then ramifies
outward through haversian and Volkmann's canals to supply the cortex. Extensive
vessels in the periosteum, the membrane surrounding the bone, supply the
superficial layers of the cortex and connect with the nutrient-artery system.
In the event of obstruction of the nutrient artery, periosteal vessels are
capable of meeting the needs of both systems. The epiphyses are supplied by a
separate system that consists of a ring of arteries entering the bone along a
circular band between the growth plate and the joint capsule. In the adult
these vessels become connected to the other two systems at the
metaphyseal-epiphyseal junction, but while the growth plate is open there is no
such connection, and the epiphyseal vessels are the sole source of nutrition
for the growing cartilage; hence they are essential for skeletal growth. |
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Drainage of blood is by a system of veins that runs
parallel with the arterial supply and by veins leaving the cortical periosteum
through muscle insertions. Muscle contraction milks blood outward, giving rise
to a centrifugal pattern of flow from the axial nutrient artery through the
cortex and out through muscle attachments. |
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| 14.4.5 |
Remodeling, growth, and development |
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Whereas renewal in tissues such as muscle occurs largely at a molecular level,
renewal of bone occurs at a tissue level and is similar to the Remodeling of
buildings in that local removal (resorption) of old bone must precede new bone
deposition. Remodeling is most vigorous during the years of active growth,
when deposition predominates over resorption. Thereafter Remodeling gradually
declines, in humans until about age 35, after which its rate remains unchanged
or increases slightly. From the fourth decade on, resorption exceeds formation,
resulting in a 5-10 percent loss in bone mass per decade, equivalent to a daily
loss of 15-30 milligrams of calcium. |
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Except for the addition of the ossification mechanisms
within cartilage, growth and development involve exactly the same type of
Remodeling as that in the adult skeleton. Both require continuous, probably
irreversible differentiation of osteoclasts and osteoblasts from the
undifferentiated bone mesenchyme. Life span of osteoclasts is from a few hours
to at most a few days, that of osteoblasts a few days to at most a few weeks. |
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Resorption is produced by clusters of osteoclasts that either erode free bone
surfaces or form "cutting cones" that tunnel through compact bone and create
the cylindrical cavities that may be subsequently filled by osteons.
Osteoclastic cells secrete enzymes and hydrogen ions onto the bone surface,
dissolving the mineral and digesting the matrix at virtually the same moment.
The process is associated with locally augmented blood flow and with a greater
surface acidity than elsewhere in bone, despite the fact that the process of
dissolving apatite consumes hydrogen ions. Resorption is usually a much more
rapid process than formation. Osteoclastic cutting cones have been observed to
advance at rates up to 500 microns per day (one micron = 1 10-3 millimetre). |
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Bone is formed on previously resorbed surfaces by
deposition of a protein matrix material (osteoid) and its subsequent
mineralization. Osteoblasts elaborate matrix as a continuous membrane covering
the surface on which they are working at a linear rate that varies with both
age and species but which in large adult mammals is on the order of 1.0 micron
per day. The unmineralized matrix constitutes an osteoid seam or border,
averaging 6 to 10 microns in thickness during active bone formation. The
biochemical and physical sequence of events that prepare matrix for
mineralization includes intracellular biosynthesis of collagen by osteoblasts,
extrusion of collagen extracellularly in soluble form, maturation or
polymerization of collagen into an array of fibrils (in random orientation in
rapidly deposited bone, in a highly ordered, regular pattern in slowly formed
lamellar bone), binding of calcium to collagen fibrils, and formation of
protein-mucopolysaccharide complexes. Mineralization itself depends upon
establishment of crystal nuclei within the matrix; this process requires five
to ten days and is under the control of the osteoblast, but its exact chemistry
is obscure. A suitable nucleating configuration is somehow established, and
once nuclei reach a critical size further mineralization proceeds spontaneously
in the presence of usual body fluid calcium and phosphorus concentrations.
Other collagenous tissues, such as dermis, tendon, and ligament, do not
normally calcify, even though bathed by the same body fluids as bone. Although
extracellular fluid is a highly supersaturated solution with respect to
hydroxylapatite, calcium and phosphorus will not spontaneously precipitate in
this crystalline form at normal physiological pH, so that one and the same
fluid is indefinitely stable in non-bone-forming regions yet richly supports
mineralization in the presence of suitable crystal nuclei. Mineral movement
into new bone is initially rapid and in compact cortical bone is known to reach
approximately 70 percent of full mineralization within a few hours after matrix
nucleation. This mineral deposition involves replacement of the water that
occupied half the original matrix volume. As water content falls, further
mineral diffusion is impeded; and the final mineralization occurs progressively
more slowly over a period of many weeks. In normal adult humans new bone
formation takes up about 400 milligrams of calcium per day, an amount
approximately equal to that in the circulating blood. |
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Osteocytes, once thought of as resting cells, are now
recognized to be metabolically active and to possess, at least in latent form,
the ability to resorb and reform bone on their lacunar walls. Although
osteocytes constitute only a small fraction of total bone volume, they are so
arranged within bone, and the network of their protoplasmic extensions is so
extensive that there is essentially no volume of bony material situated more
than a fraction of a micron from a cell or its processes. Of the more than
1,200 square metres (1,435 square yards) of anatomic surface within the
skeleton of an adult man, about 99 percent is accounted for by the lacunar and
canalicular surfaces. Resorption and deposition on this surface serve both to
regulate plasma-calcium concentration and to renew bony material. This renewal
may be particularly important because all composite materials change in their
physical properties with time. It is not known whether bone properties change
sufficiently to have biologic consequence, but to the extent that such change
does occur, renewal around osteocytes would provide for the physical
maintenance of bone structural material. |
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| 14.4.6 |
Types of bone formation |
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Bone is formed in the embryo in two general ways.
For most bones the general shape is first laid down as a cartilage model, which
is then progressively replaced by bone (endochondral bone formation). A few
bones (such as clavicle and calvarium) develop within a condensed region of
fibrous tissue without a cartilaginous intermediate (membrane bone formation).
In long bones a collar of spongy membrane bone is first laid down in the
fibrous tissues surrounding the cartilaginous model of the shaft. At the same
time the cartilage deep to this collar begins to degenerate and calcify. The
bone is then penetrated by blood vessels, which grow into the degenerating
model and remove the calcified cartilage enclosed within the collar. Vascular
invasion proceeds toward both ends of the model in parallel with continued
extension of the bony collar. This leaves a structure consisting of two
cartilaginous epiphyses at the ends of a hollow, bony shaft. |
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Growth from this point on is accomplished in two
ways. Radial growth occurs by deposition of new bone on the periosteal surface
and roughly equivalent resorption at the endosteal surface. Longitudinal growth
involves replacement of cartilage by bone from the shaft side of the growth
plate, at a rate closely matched to the production of new cartilage by the
plate itself. The growth plate consists of highly ordered rows of cartilage
cells; the row farthest removed from the bony shaft is a basal or germinal
layer; it is responsible for cell replication and cartilage growth. The complex
sequence of longitudinal growth consists of cartilage cell degeneration
farthest from the germinal layer, calcification of cartilage in that area,
deposition over it of a thin layer of true bone (primary spongiosa), and,
finally, osteoclastic resorption to extend the medullary cavity in parallel
with longitudinal growth and to reshape the contour of the shaft. |
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Cartilage growth, degeneration, calcification, and
ultimate replacement by bone is responsible for most growth in length in
vertebrates. It first begins in the embryo and continues until full skeletal
maturity, when in most species the growth plates fuse and disappear. |
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The appearance of epiphyseal ossification centres
and their ultimate fusion, both of which can be detected by ordinary X-rays,
normally follows an orderly and predictable sequence that is of great value in
the evaluation of disorders of growth and development. Because of the
complicated interaction of several tissue elements in the process of
endochondral ossification, the metaphyseal region of bones is the seat of, or
prominently reflects, many nutritional or metabolic disturbances of growth.
Examples of disorders involving this growth mechanism include rickets and
achondroplastic dwarfism. |
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| 14.4.7 |
Hormonal influences |
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The most striking effects of estrogens are seen in birds, in which during the
part of the cycle prior to egg formation a marked increase in osteoblastic
activity occurs along the inside surfaces of the long bones, and the medullary
cavities become filled with spongy bone. As the egg is formed, this spongy bone
is rapidly resorbed, plasma calcium rises dramatically, and calcium is
deposited in the shell. In mammals studied prior to skeletal maturity,
administration of estrogens produces an accelerated appearance of ossification
centres, a slowing in growth of cartilage and bone, and fusion of the
epiphyses; the result is an adult skeleton smaller than normal. In older
mammals estrogens in certain dosages and schedules of administration may
inhibit trabecular bone resorption, and in some species prolonged
administration of estrogen may lead to increased bone porosity. In
postmenopausal women administration of estrogen suppresses bone resorption and
produces a transient decrease in serum calcium and phosphorus and in renal
reabsorption of phosphorus, as well as positive calcium balance, effects which
help to stabilize the total skeletal bone mass. |
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The effects described are for estrogens as a general class of steroid hormone,
and no attempt has been made to differentiate between the actions of natural
estrogenic hormones and the many synthetic varieties now in wide use to
suppress ovulation. Extremely few studies have been conducted to determine the
effects of the latter on bone. |
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Very little is known of the effects of progesterone on
bone beyond studies in young guinea pigs suggesting slight inhibition of the
activity of such hormones as estrogens, which speed skeletal development. |
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In mammals, including humans, just prior to sexual
maturity, the growth spurt occurring in males is attributable principally to
the growth-promoting action of the male sex hormone testosterone. When
administered, testosterone and related steroids stimulate linear growth for a
limited period; ultimately, however, particularly if they are given in large
doses, they suppress bone growth as the result of hastened skeletal development
and premature epiphyseal closure. Studies have indicated that testosterone
derivatives administered to adult mammals suppress the turnover and resorption
of bone and increase the retention of nitrogen, phosphorus, and calcium. |
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The influence of the adrenal corticosteroid hormones on bone is varied, but the
principal result is slowing of growth in the young and decrease in bone mass in
the adult. In Cushing's syndrome, in which there is abnormally high secretion
of corticosteroids, bone loss to the point of fractures often occurs. Cortisol
in high concentration suppresses protein and mucopolysaccharide synthesis, with
inhibition of bone matrix formation and of incorporation of nucleosides into
bone cells. |
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Lack of the internal secretion of the thyroid gland results in retardation of
skeletal growth and development. Action of this hormone to facilitate growth
and skeletal maturation is probably indirect, through its general effects on
cell metabolism. Thyroid hormone in excess leads in the young to premature
appearance of ossification centres and closure of the epiphyses, and in the
adult to increased bone-cell metabolism. Commonly in the hyperthyroid adult
bone resorption predominates over increased bone formation with resultant loss
of bone mass. |
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The anterior lobe of the pituitary gland secretes a hormone essential for
growth and development of the skeleton. This effect of the hormone is indirect
and mediated by "sulfation factor," a substance produced in the liver in
response to stimulation by the growth hormone. The extent to which growth
hormone is involved in skeletal remodelling in the adult is not known, but
excessive elaboration of the hormone after maturity leads to distorted
enlargement of all bones in the condition known as acromegaly. Excessive
elaboration of growth hormone prior to epiphyseal closure leads to gigantism.
Studies of the administration of growth hormone to man have indicated marked
species specificity; growth in hypopituitary dwarfs is stimulated only by human
or primate growth hormone. The principal metabolic effects in man of the
hormone are retention of nitrogen and increased turnover of calcium, resulting
in increases both in intestinal calcium absorption and in urinary calcium
excretion. |
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Insulin participates in the regulation of bone growth; it may enhance or even
be necessary for the effect of growth hormone on bone. Insulin has been found
to stimulate growth and epiphyseal widening in rats whose pituitaries have been
removed and to promote chondroitin sulfate synthesis in cartilage and bone and
the transport of amino acids and nucleosides into bone. |
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